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Practice guideline for the treatment of familial amyloid polyneuropathy

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dc.contributor.author Carretero, Marcelina
dc.contributor.author Sáez, María S.
dc.contributor.author Posadas Martínez, María L.
dc.contributor.author Aguirre, María A.
dc.contributor.author Sorroche, Patricia
dc.contributor.author Negro, Agustina
dc.contributor.author Calandra, Cristian R.
dc.contributor.author Salutto, Valeria L.
dc.contributor.author Lautre, Andrea Rosana
dc.contributor.author Conti, Eugenia
dc.contributor.author León Cejas, Luciana
dc.contributor.author Reisin, Ricardo C.
dc.contributor.author Nucifora, Elsa M.
dc.contributor.author Rugiero, Marcelo
dc.date.accessioned 2023-01-04T12:20:13Z
dc.date.available 2023-01-04T12:20:13Z
dc.date.issued 2022
dc.identifier.citation Carretero M, Sáez MS, Posadas Martínez ML, Aguirre MA, Sorroche P, Negro A, Calandra CR, Salutto V, Lautre A, Conti E, León Cejas L, Reisin RC, Nucifora EM, Rugiero M. Guía de práctica clínica de tratamiento de la polineuropatía amiloidótica familiar [Practice guideline for the treatment of familial amyloid polyneuropathy]. Medicina (B Aires). 2022;82(2):262-274. es_ES
dc.identifier.uri https://www.medicinabuenosaires.com/PMID/35417391.pdf
dc.identifier.uri https://repositorio.fleni.org.ar/xmlui/handle/123456789/756
dc.description.abstract This clinical practice guideline for the treatment of familial amyloid polyneuropathy is based on the best available evidence of clinical effectiveness. A list of questions was generated with a PICO format focused on the effectiveness and safety of the treatment of familial amyloid polyneuropathy. The search was carried out in PubMed, Cochrane and Epistemonikos. The levels of evidence and grades of recommendation were based on the GRADE system. Recommendations were graded according to their direction and their strength and were evaluated with the GLIA tool for their implementation. In patients with familial amyloid polyneuropathy and stage I and II neuropathy, it is suggested: inotersen 300 mg subcutaneous weekly or patisirán 0.3 mg/kg intravenously once every 3 weeks, since they probably stabilize or slow the progression of neuropathy and worsening quality of life (moderate quality of evidence; strength of recommendation weak). In patients with familial amyloid polyneuropathy and stage I neuropathy, treatment with tafamidis 20 mg orally, once a day, is suggested, as it could slow the progression of neuropathy and worsen quality of life (low quality of evidence; strength of recommendation weak). In patients with familial amyloid polyneuropathy and symptomatic neuropathy and in the absence of other treatments with approved efficacy, treatment with oral diflunisal 250 mg twice daily is suggested, as it could prevent the progression of neuropathy (quality evidence low; strength of recommendation weak). es_ES
dc.language.iso spa es_ES
dc.publisher Fundación Revista Medicina (Buenos Aires) es_ES
dc.rights info:eu-repo/semantics/openAccess
dc.rights.uri https://creativecommons.org/licenses/by/2.5/ar/
dc.subject Amyloid Neuropathies es_ES
dc.subject Neuropatías Amiloides es_ES
dc.subject Practice Guideline es_ES
dc.subject Guía de Práctica Clínica es_ES
dc.title Practice guideline for the treatment of familial amyloid polyneuropathy es_ES
dc.type info:eu-repo/semantics/article es_ES
dc.type info:eu-repo/semantics/publishedVersion
dc.description.fil Fil: Lautre, Andrea Rosana. Fleni. Departamento de Neurología. Sección de Neurofisiología; Argentina.
dc.description.fil Fil: Carretero, Marcelina. Hospital Italiano de Buenos Aires; Argentina.
dc.description.fil Fil: Sáez, María S. Hospital Italiano de Buenos Aires; Argentina.
dc.description.fil Fil: Posadas Martínez, María L. Hospital Italiano de Buenos Aires; Argentina.
dc.description.fil Fil: Aguirre, María A. Hospital Italiano de Buenos Aires; Argentina.
dc.description.fil Fil: Sorroche, Patricia. Hospital Italiano de Buenos Aires; Argentina.
dc.description.fil Fil: Negro, Agustina. Hospital Italiano de Buenos Aires; Argentina.
dc.description.fil Fil: Calandra, Cristian R. Hospital de Alta Complejidad El Cruce; Argentina.
dc.description.fil Fil: Salutto, Valeria. Instituto de Investigaciones Médicas Alfredo Lanari; Argentina.
dc.description.fil Fil: Conti, Eugenia. Hospital Británico; Argentina.
dc.description.fil Fil: León Cejas, Luciana. Hospital Británico; Argentina.
dc.description.fil Fil: Reisin, Ricardo C. Hospital Británico; Argentina.
dc.description.fil Fil: Nucifora, Elsa M. Hospital Italiano de Buenos Aires; Argentina.
dc.description.fil Fil: Rugiero, Marcelo. Hospital Italiano de Buenos Aires; Argentina.
dc.relation.ispartofVOLUME 82
dc.relation.ispartofNUMBER 2
dc.relation.ispartofPAGINATION 262-274.
dc.relation.ispartofCOUNTRY Argentina
dc.relation.ispartofCITY Buenos Aires
dc.relation.ispartofTITLE Medicina (Buenos Aires)
dc.relation.ispartofISSN 1669-9106
dc.type.snrd info:ar-repo/semantics/artículo es_ES


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